kukaus
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A sample of glycogen from a newborn with liver disease is incubated with inorganic phosphate, normal glycogen phosphorylase and debranching enzyme. the ratio of glucose 1 phosphate to glucose formed in this reaction is abnormally high. the patient is most likely deficient in which of the following:
a) alpha -1,6- glucosidase
b) alpha 1,4--->alpha 1,4 glucan transferase
c) alpha 1,4--->alpha 1,6 glucan ttransferase
d) glycogen phosphorylase
e) glycogen phosphorylase kinase
your choice with explanation please
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| Kalyann
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From where is this question ?
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I will do it for you, my love...
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| kukaus
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kaplan qbank, new one.
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| pr20
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c) alpha 1,4--->alpha 1,6 glucan ttransferase
The ratio of glucose-1-phosphate to free glucose reflects the number of glucose residues(released as glucose-1-phosphate)between branch points(free glucose released)in the glycogen.
High glucose-1-phosphate:free glucose ratio indicates that glycogen has fewer than normal branches suggesting a branching enzyme deficiency.
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| kukaus
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thats correct
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