"peekay" wrote:
BUT HOW WOULD U APPLY THIS PNEUMONICS FOR ENZYMES WHICH ARE DEFICENT, SINCE QUESTIONS MOST QS ARE ABOUT THEIR NAMES
The mnemonics was just to help us remember the Glycogen storage diseases.
For POMPE's- First iad suggests that: POMPe's trashes the PUMP (cardiomegaly) due to lysosomal 1,4 glucosidase.
For HERS Disease- its HEpatic glycogen phosphorylase deficiency
For Mc Ardles- its Muscle Glycogen phosphorylase def.
For the other enzyme , we just have to memorize, sorry :roll:
PS: Theres another Glucogen storage dse: ANDERSEN Disease(Amylopectinosis) defiency of branching enzyme. Causing short outer branches of glycogen.
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| peekay
Forum Guru
Topics: 102
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THANK YOU IT IS EASY NOW.
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| usmleasr
Forum Guru
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anderson's is special in that ..all others are defect in glycogenolysis..but anderson is the only disease of glycogen synthesis
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| usmle prep
Forum Senior
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good discussion guys!!!
i feel more confident and motivated to study,after joining this forum!!!
thanx to all of u..
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| bright_nnn
Forum Senior
Topics: 17
Posts: 97
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This is a good way to remember=Anderson(only Synthesizing defect)
Von Gierke=Glucose 6 phosphatase
Pompe=Lysosomal Alpha 1 4 Glucosidase
Mc Ardles=Muscle Glycogen Phosphorylase
Hers =Hepatic Glycogen Phosphrylase
Cori=Alpha 1 6 Glucosidase
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