new_n_lost
Politically InCorrect
Topics: 653
Posts: 6,085
|
A Guatemalan child with a history of meconium ileus is brought to a clinic because of a chronic cough. The mother notes a history of respiratory tract infections and bulky, foul-smelling stools. After assessment of the respiratory tract illness, the physician should also look for signs of
A. cystinuria
B. hypoglycemia
C. iron deficiency anemia
D. sphingomyelin accumulation
E. vitamin A deficiency
Edited by new_n_lost on 03/24/07 - 03:45 PM
___________________
FORUM RULES-- Those who believe in telekinesis, raise my hand. I get enough exercise just by pushing my luck --P4U World.." The pure and simple truth is rarely pure and never simple."
|
| mms
Forum Junior
Topics: 1
Posts: 72
|
E.
Because of inadequate absorbtion of liposolubles vit. in cystic fibrosis 
|
| Aashi
Forum Moderator
Topics: 113
Posts: 1,028
|
Cystic fibrosis------->GI S/S--->fat malabsorption --->vit ADEK def-------->E
___________________
"Obstacles are those frightful things you see when you take your EYES off your goal."
|
| usmle4me
Forum Elite
Topics: 6
Posts: 283
|
E
|
| new_n_lost
Politically InCorrect
Topics: 653
Posts: 6,085
|
___________________
FORUM RULES-- Those who believe in telekinesis, raise my hand. I get enough exercise just by pushing my luck --P4U World.." The pure and simple truth is rarely pure and never simple."
|
| new_n_lost
Politically InCorrect
Topics: 653
Posts: 6,085
|
The correct answer is E. The child is likely suffering from cystic fibrosis. In this disorder, an abnormality of chloride channels causes all exocrine secretions to be much thicker, and more viscous than normal. Pancreatic secretion of digestive enzymes is often severely impaired, with consequent steatorrhea and deficiency of fat-soluble vitamins, including vitamin A.
Cystinuria (choice A) is a relatively common disorder in which a defective transporter for dibasic amino acids (cystine, ornithine, lysine, arginine; COLA) leads to saturation of the urine with cystine, which is not very soluble in urine, and precipitates out to form stones.
Hypoglycemia (choice B) is not a prominent feature of children with cystic fibrosis who are on a normal diet. Hyperglycemia may occur late in the course of the disease.
Iron deficiency anemia (choice C) is not found with any regularity in children with cystic fibrosis.
Sphingomyelin accumulation (choice D) is generally associated with deficiency of sphingomyelinase, as seen in Niemann-Pick disease.
___________________
FORUM RULES-- Those who believe in telekinesis, raise my hand. I get enough exercise just by pushing my luck --P4U World.." The pure and simple truth is rarely pure and never simple."
|
| dannyridelman
Forum Newbie
Topics: 1
Posts: 9
|
except i live in guatemala and CF is extremely rare here. is this was a real pt, i would look for Fe def anemia, as 80% of kids here have it... sad but true...
|
| Addicudo
Forum Guru
Topics: 124
Posts: 608
|
___________________
... Idle hands are the DeVilS play ground ...
|
|
| |
| | | | | | | | |
